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Rhabdomyomatous mesenchymal
hamartoma is a rare congenital lesion of the dermis and soft tissues.
This
entity exists under various names including striated muscle hamartoma,
congenital midline hamartoma, and hamartoma of cutaneous adnexa and
mesenchyme.
Age:
Usually presents in neonates or infants. Cases have been reported in
adults.
Site:
Presents as one or more small cutaneous polyps in the head and neck
region.
Microscopic features:
The lesion consists of a disordered and varied
collection of mature adipose tissue, skeletal muscle, adnexal elements and
nerve bundles.
Bundles of
skeletal muscle is present in the reticular dermis which may extend into
the subcutis.
This lesion may be
associated with other congenital anomalies and anomaly syndromes hence
systemic evaluation of patients diagnosed with this entity has been
recommended.
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