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Pulmonary Pathology Online

Pathology of Neurogenic Tumours of the Lung

 Dr Sampurna Roy MD




Primary intrapulmonary neurogenic tumours are extremely rare.

Majority of pulmonary neurogenic sarcomas have a history of neurofibromatosis and some may arise de novo.

Tumours showing features of schwannoma are designated as malignant peripheral nerve sheath tumor (MPNST).

These may present as endobronchial masses or nodules within lung parenchyma without any connection to the bronchial tree.

Histologically, the tumours are composed of spindle cells, most often arranged in "herringbone" pattern.

Rarely, these tumors may show rhabdomyoblastic differentiation in association with neural elements and are designated as malignant "triton" tumors.

The diagnosis is reliably confirmed by immunohistochemistry and ultrastructural examination.

Visit: Schwannoma (neurilemmoma)and variants ; Neurofibroma and variants; Perineurioma ;Dermal nerve sheath myxoma; Cellular neurothekeoma ;Malignant peripheral nerve sheath tumour


Further reading:

Primary pulmonary tumours of neurogenic origin.

Primary malignant peripheral nerve sheath tumor of the lung in a young child without neurofibromatosis type 1

Primary pulmonary tumours of nerve sheath origin.

Endobronchial neurogenic tumors .

Massive hemoptysis caused by endobronchial schwannoma in a patient with neurofibromatosis 2.

A rare endobronchial neurilemmoma (Schwannoma).

A rare case of a primary intrabronchial neurofibroma

Triton's malignant intrapulmonary tumor.

Primary malignant 'triton' tumour of the lung.

A case of pulmonary neurilemmoma.

A case of primary intrapulmonary neurilemoma and review of the literature.



Dr Sampurna Roy  MD

Consultant  Histopathologist (Kolkata - India)







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